{"created":"2023-06-20T15:50:39.324922+00:00","id":3524,"links":{},"metadata":{"_buckets":{"deposit":"2c730f18-abe1-4a7d-bd65-88402991bd65"},"_deposit":{"created_by":18,"id":"3524","owners":[18],"pid":{"revision_id":0,"type":"depid","value":"3524"},"status":"published"},"_oai":{"id":"oai:redcross.repo.nii.ac.jp:00003524","sets":["99:64:119"]},"author_link":["93","6885","256","380","8084","192","8423","129","8109"],"item_5_biblio_info_7":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2004-03-01","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"1","bibliographicPageEnd":"96","bibliographicPageStart":"92","bibliographicVolumeNumber":"9","bibliographic_titles":[{"bibliographic_title":"徳島赤十字病院医学雑誌"},{"bibliographic_title":"Tokushima Red Cross Hospital Medical Journal","bibliographic_titleLang":"en"}]}]},"item_5_description_5":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"慢性肥厚性硬膜炎の65歳,女性例を報告した.患者は嗄声・嚥下障害で発症し,順次顔面神経麻痺,眼球運動障害などの脳神経症状が上行拡大した後,意識障害を呈した.血液検査では炎症所見があり,抗核抗体,リウマチ因子,p-ANCA等の自己抗体が陽性であった.髄液検査では細胞数19/3㎜3,蛋白272mg/dl と増加していた.頭部MRI ではT1強調\r\nでわずかに肥厚した硬膜が観察され,Gdにより造影を行うと著明に肥厚した脳硬膜が観察された.肥厚性硬膜炎と診断し,直ちにステロイドパルス療法を行った.意識障害は間もなく回復し,脳神経の麻痺も眼球運動から順次改善した.2回目のパルス療法を行ったが,直後に下血,膿胸を来たしたため,それ以上の治療は断念した.殆ど全ての脳神経症状は改善したが,嗄声,嚥下障害は残った.本例は各種の自己抗体が陽性であり,ステロイドが著効を示したことより,その発症に自己免疫の関与が強く示唆された.原因の明らかでない脳神経症状をみた場合,本症も考慮に入れ速やかに造影MRI を行うことが必要である.","subitem_description_type":"Abstract"}]},"item_5_full_name_3":{"attribute_name":"著者別名","attribute_value_mlt":[{"nameIdentifiers":[{"nameIdentifierScheme":"WEKO"}],"names":[{"name":"MIHARA, 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