{"created":"2023-06-20T15:59:52.549968+00:00","id":18000,"links":{},"metadata":{"_buckets":{"deposit":"cbb28831-9fa3-412e-97ac-3d08a4e547b9"},"_deposit":{"created_by":41,"id":"18000","owners":[41],"pid":{"revision_id":0,"type":"depid","value":"18000"},"status":"published"},"_oai":{"id":"oai:redcross.repo.nii.ac.jp:00018000","sets":["340","340:341","340:341:648"]},"author_link":["68460","68461","68459","68457","68462","68458"],"item_10001_biblio_info_7":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2022-04-15","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"1","bibliographicPageEnd":"54","bibliographicPageStart":"49","bibliographicVolumeNumber":"25","bibliographic_titles":[{"bibliographic_title":"高知赤十字病院医学雑誌"},{"bibliographic_title":"Medical Journal of Japanese Red Cross Kochi Hospital","bibliographic_titleLang":"en"}]}]},"item_10001_description_5":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"脳表ヘモジデリン沈着症(superficial siderosis:SS)は,鉄(ヘモジデリン)が脳表や脊髄表面,\n脳実質に沈着し,神経障害を来す稀な神経変性疾患であり,小脳・脳幹などの後頭蓋窩や脊髄を中心\nにびまん性・対称性に病変が生じる古典型 SS と限局性に病変が生じる限局型 SS の2種類がある.本\n邦では SS の診断基準が作成され,SS が指定難病となったことで,SS が徐々に認知されてきているが,\n古典型 SS では感音性難聴や小脳失調等の症状が進行して ADL の低下を生じるため,早期発見・早\n期治療が重要であると思われるが,未だその病態は充分に解明されておらず,治療法も確立していな\nい.今回我々は脳ドックで発見された SS の 1 例を経験した.MRI の発達により今後は今回の症例の\nように SS が偶然に発見される機会が増えると思われ,SS という疾患を認知して,発症前や発症早期\nの症例することが,病態解明や治療方針の確立に役立つと思われる.","subitem_description_type":"Abstract"}]},"item_10001_publisher_8":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"高知赤十字病院"}]},"item_10001_rights_15":{"attribute_name":"権利","attribute_value_mlt":[{"subitem_rights":"高知赤十字病院"}]},"item_10001_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"0919-7427","subitem_source_identifier_type":"ISSN"}]},"item_10001_version_type_20":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"泉谷, 智彦"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"佐原, 和真"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"板東, 康司"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"羽星, 辰哉"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"松下, 展久"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"鈴江, 淳彦"}],"nameIdentifiers":[{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2022-04-15"}],"displaytype":"simple","filename":"脳ドックで発見された脳表ヘモジデリン沈着症の1 例.pdf","filesize":[{"value":"4.5 MB"}],"format":"application/pdf","licensetype":"license_9","mimetype":"application/pdf","url":{"label":"高知赤十字病院医学雑誌Vol.25-15","url":"https://redcross.repo.nii.ac.jp/record/18000/files/脳ドックで発見された脳表ヘモジデリン沈着症の1 例.pdf"},"version_id":"56d35be2-928c-4762-95b6-93a1f85430b9"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"脳表ヘモジデリン沈着症","subitem_subject_scheme":"Other"},{"subitem_subject":"MRI","subitem_subject_scheme":"Other"},{"subitem_subject":"T2* 強調画像","subitem_subject_scheme":"Other"},{"subitem_subject":"感音性難聴","subitem_subject_scheme":"Other"},{"subitem_subject":"小脳失調","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"脳ドックで発見された脳表ヘモジデリン沈着症の 1例","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"脳ドックで発見された脳表ヘモジデリン沈着症の 1例"}]},"item_type_id":"10001","owner":"41","path":["340","341","648"],"pubdate":{"attribute_name":"公開日","attribute_value":"2022-04-15"},"publish_date":"2022-04-15","publish_status":"0","recid":"18000","relation_version_is_last":true,"title":["脳ドックで発見された脳表ヘモジデリン沈着症の 1例"],"weko_creator_id":"41","weko_shared_id":-1},"updated":"2023-06-20T17:48:51.761426+00:00"}