{"created":"2023-06-20T15:59:44.439605+00:00","id":17766,"links":{},"metadata":{"_buckets":{"deposit":"1c463cd7-b0ac-4d9d-9748-c9a90dd83004"},"_deposit":{"created_by":22,"id":"17766","owners":[22],"pid":{"revision_id":0,"type":"depid","value":"17766"},"status":"published"},"_oai":{"id":"oai:redcross.repo.nii.ac.jp:00017766","sets":["100:90:640"]},"author_link":["67478","67479","67476","67477","67481","67474","60416","67480","67475"],"item_5_biblio_info_7":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2020-12","bibliographicIssueDateType":"Issued"},"bibliographicPageEnd":"97","bibliographicPageStart":"90","bibliographicVolumeNumber":"41","bibliographic_titles":[{"bibliographic_title":"京都第二赤十字病院医学雑誌"},{"bibliographic_title":"Medical journal of Kyoto Second Red Cross Hospital","bibliographic_titleLang":"en"}]}]},"item_5_description_5":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"症例は、76歳女性。咳嗽、労作時呼吸困難で近医受診、上気道炎として加療後、低酸素血症をきたし京都第二赤十字病院呼吸器内科へ紹介された。胸部CTで胸膜直下、気管支血管束周囲に広範なconsolidation、すりガラス影を認めた。筋症状を伴わず、特徴的な皮疹を認め、臨床的無筋症性皮膚筋炎に伴う急速進行性間質性肺炎と診断した。入院後ステロイド、シクロスポリンで加療したが改善なく、第8病日に抗MDA5抗体陽性が判明し、シクロフォスファミドパルス療法、第14病日から血漿交換療法を併用したが改善なく、第29病日に永眠された。本症例は入院時に重度の呼吸不全を認め、入院直後から集学的治療を行っても救命は困難と考えられた。しかし、呼吸不全が軽度で画像上の肺障害が少ない症例で集学的治療の有効性を示す報告もあり、本疾患が疑われる軽症例では抗MDA5抗体の結果を待たずに集学的治療の検討が必要と考えられた。","subitem_description_type":"Abstract"}]},"item_5_full_name_3":{"attribute_name":"著者別名","attribute_value_mlt":[{"nameIdentifiers":[{"nameIdentifierScheme":"WEKO"}],"names":[{"name":"KIMURA, Taku"}]}]},"item_5_publisher_8":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"京都第二赤十字病院"}]},"item_5_source_id_11":{"attribute_name":"書誌レコードID","attribute_value_mlt":[{"subitem_source_identifier":"AN00357778 ","subitem_source_identifier_type":"NCID"}]},"item_5_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"0389-4908","subitem_source_identifier_type":"ISSN"}]},"item_5_version_type_20":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"木村, 拓"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"廣瀬, 和紀"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"國松, 勇介"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"谷, 望未"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"佐藤, いずみ"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"小倉, 由莉"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"瀬野, 真文"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"竹田, 隆之"}],"nameIdentifiers":[{},{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2021-05-13"}],"displaytype":"simple","filename":"MJKSRCH41_90.pdf","filesize":[{"value":"707.7 kB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"kyo2_000123","url":"https://redcross.repo.nii.ac.jp/record/17766/files/MJKSRCH41_90.pdf"},"version_id":"1bbdf80e-3cea-49a8-8a7b-ea1aec2e30da"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"自己抗体","subitem_subject_scheme":"Other"},{"subitem_subject":"皮膚筋炎","subitem_subject_scheme":"Other"},{"subitem_subject":"呼吸不全","subitem_subject_scheme":"Other"},{"subitem_subject":"胸部CT","subitem_subject_scheme":"Other"},{"subitem_subject":"高齢者","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"technical report"}]},"item_title":"抗MDA5抗体陽性の急速進行性間質性肺炎に対して血漿交換療法を含めた集学的治療を行った1例","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"抗MDA5抗体陽性の急速進行性間質性肺炎に対して血漿交換療法を含めた集学的治療を行った1例"},{"subitem_title":"A case of anti-MDA5 antibody-positive rapidly progressive interstitial lung disease treated with multidisciplinary therapy including plasma exchange","subitem_title_language":"en"}]},"item_type_id":"5","owner":"22","path":["640"],"pubdate":{"attribute_name":"公開日","attribute_value":"2021-05-13"},"publish_date":"2021-05-13","publish_status":"0","recid":"17766","relation_version_is_last":true,"title":["抗MDA5抗体陽性の急速進行性間質性肺炎に対して血漿交換療法を含めた集学的治療を行った1例"],"weko_creator_id":"22","weko_shared_id":-1},"updated":"2023-06-20T17:55:04.352342+00:00"}