{"created":"2023-06-20T15:59:37.068418+00:00","id":17583,"links":{},"metadata":{"_buckets":{"deposit":"3411153e-f142-4d6f-8dc0-be6634348fb7"},"_deposit":{"created_by":53,"id":"17583","owners":[53],"pid":{"revision_id":0,"type":"depid","value":"17583"},"status":"published"},"_oai":{"id":"oai:redcross.repo.nii.ac.jp:00017583","sets":["615:616:644"]},"author_link":["66872","66875","66877","66878","66874","66876","66871","66873"],"item_10001_biblio_info_7":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2020-11-30","bibliographicIssueDateType":"Issued"},"bibliographicPageEnd":"58","bibliographicPageStart":"54","bibliographicVolumeNumber":"31","bibliographic_titles":[{"bibliographic_title":"岡山赤十字病院医学雑誌"},{"bibliographic_title":"The Okayama Red Cross Hospital Journal of Medicine","bibliographic_titleLang":"en"}]}]},"item_10001_description_5":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"症例1 は44歳の女性.既往は無く,家族歴で父親に大動脈解離と父方の叔母に大動脈解離\nを指摘されていた.2015年1 月に胸背部痛を主訴に当院救急外来を受診し,造影CT にて上\n行大動脈から総腸骨動脈までの偽腔開存型Stanford A の急性大動脈解離を認めた.大動脈置\n換術を施行され退院された.\n症例2 は46歳の女性.症例1 の姉.既往は無く,2018年10月に数日前からの背部痛を主訴\nに当院紹介となった.造影CT にて偽腔開存型Stanford A の急性大動脈解離を認め,大動脈\n置換術施行され退院された.\n症例3 は42歳の男性.症例1 の弟.既往は無く,背部痛を主訴に救急搬送となり,急性大\n動脈解離に対して大動脈置換術施行され退院された.\n症例2 で家族性大動脈瘤/解離の原因遺伝子として報告のある平滑筋αアクチン遺伝子変\n異(ACTA2)が認められた.","subitem_description_type":"Abstract"}]},"item_10001_publisher_8":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"The Okayama Red Cross Hospital Journal of Medicine"}]},"item_10001_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"0915-8073","subitem_source_identifier_type":"ISSN"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"越智, 正彦"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"田中, 正道"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"大道, 俊介"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"川北, 祝史"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"大澤, 和宏"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"湯本, 晃久"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"齋藤, 博則"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"福家, 聡一郎"}],"nameIdentifiers":[{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2020-12-10"}],"displaytype":"simple","filename":"04-5 症例 越智 p.54-58.pdf","filesize":[{"value":"12.0 MB"}],"format":"application/pdf","licensetype":"license_11","mimetype":"application/pdf","url":{"label":"okayama000035","url":"https://redcross.repo.nii.ac.jp/record/17583/files/04-5 症例 越智 p.54-58.pdf"},"version_id":"906f43df-e312-4fa8-a39d-1cfe7419fff7"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"Familial thoracic aortic dissection","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"genetics","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"ACTA2","subitem_subject_language":"en","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"家族性大動脈解離の一家系","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"家族性大動脈解離の一家系"},{"subitem_title":"A family line with familial aortic dissection","subitem_title_language":"en"}]},"item_type_id":"10001","owner":"53","path":["644"],"pubdate":{"attribute_name":"公開日","attribute_value":"2021-02-01"},"publish_date":"2021-02-01","publish_status":"0","recid":"17583","relation_version_is_last":true,"title":["家族性大動脈解離の一家系"],"weko_creator_id":"53","weko_shared_id":-1},"updated":"2023-06-20T17:57:56.191057+00:00"}